Publication 3/01/2005 Complete deficiency of the low-density lipoprotein receptor is associated with increased apolipoprotein B-100 production. Millar JS, Maugeais C, Ikewaki K, Kolansky DM, Barrett PH, Budreck EC, Boston RC, Tada N, Mochizuki S, Defesche JC, Wilson JM, Rader DJ Arteriosclerosis, Thrombosis, And Vascular Biology